Human tail is a rare congenital anomaly with a prominent lesion from the lumbosacrococcygeal region. Dao and Netsky classified this anomaly, distinguishing ‘true tail’ and ‘pseudotail’. The true tail comprises mainly mesenchymal tissues (adipose, connective, muscle, nerve tissue, blood vessels and cutis). All other protrusions are summarized as pseudotails. Tail-like appendages are frequently associated with abnormalities of the spine and spinal cord. The report presents the case of a child born with human tail containing normal and abnormal tissues (fibrolipoma). Surgical excision of the tail was performed 2 days after birth. After the operation, the patient had an uneventful convalescence and received follow-up at our outpatient clinic without neurological deficit, only high pressure bladder.